CROW-FUKASE SYNDROME, A RARE CASE: FIRST OF ITS KIND REPORTED IN A TERTIARY HOSPITAL IN MAKURDI, NIGERIA
NWANNADI IKENNA ALEXANDER *
Department of Haematology, College of Health Sciences, Benue State University, Makurdi, Nigeria
ALAO OLUSAYO OLAYINKA
Department of Haematology, College of Health Sciences, Benue State University, Makurdi, Nigeria
OKOLI ROBERTSON
Department of Haematology, College of Health Sciences, Benue State University, Makurdi, Nigeria.
ABA IYAJI HANNAH
Department of Haematology, College of Health Sciences, Benue State University, Makurdi, Nigeria
OKOLIE IFECHUKWUDI
Department of Haematology, Benue State University Teaching Hospital, Makurdi, Benue State, Nigeria
*Author to whom correspondence should be addressed.
Abstract
Crow-Fukase syndrome also known as POEMS syndrome or Takatsuki disease or PEP syndrome (Plasma cell dyscrasia, Endocrinopathy and Polyneuropathy) is a rare multisystem disorder that is associated with plasma cell neoplasm. The syndrome is made up of polyneuropathy, organomegaly, endocrinopathy, monoclonal gammamopathy, and skin changes. We report here the first case of Crow-Fukase syndrome in a five year old tertiary hospital, in the north central region of Nigeria.
Keywords: Multisystem disorder, POEMS syndrome, plasma cell dyscrasia, monoclonal gammopathy