Journal of Case Reports in Medical Science

Renal cell carcinoma (RCC) is the most common renal malignancy in adults and encompasses several variant histological subtypes, among which clear cell RCC is the most common type. RCC with rhabdoid morphology is one such rare variant with aggressive behavior. We present a case of 62 years old female patient, who got admitted with complaints of pain in the right lumbar region since one year. Ultrasound abdomen revealed large heterogeneous enlarged mass with cystic spaces measuring 9cm x 6cm arising from the lower pole of the right kidney. Initially, a provisional diagnosis of renal cell carcinoma was made and right radical nephrectomy was perfomed. Histopathological sections from the tumour revealed features of clear cell renal cell carcinoma with rhabdoid morphology, which was confirmed by immunohistochemistry. A pTNM staging of pT3a Nx Mx was assigned with morphological features.